TY - JOUR T1 - EFficacy of a nonrestricted fat diet in patients with cystic fibrosis AU - Luder E, Kattan M, Thornton JC, Koehler KM, Bonforte RJ Y1 - 1989/04/01 N1 - 10.1001/archpedi.1989.02150160084017 JO - American Journal of Diseases of Children SP - 458 EP - 464 VL - 143 IS - 4 N2 - • We sought to determine if an increased oral intake with a noninvasive nutrition program in patients with cystic fibrosis could influence growth, weight gain, and pulmonary function. Thirty-seven patients, aged 2 to 27 years, were instructed to consume a nonrestricted fat diet during an intervention period of 4 years. The results showed that patients increased the mean energy intake significantly to a level of more than 120% of the recommended daily allowance. The enhanced intake resulted in significant weight gain. Pulmonary function (forced expiratory flow25%75%) deteriorated during the 2-year preintervention period but stabilized during the 4-year intervention period. Both male and female patients were able to maintain their established height and weight scores during adolescence. The recommendation for a high-energy diet with no restrictions placed on the fat intake and the control of the steatorrhea by administration of an optimal enzyme dosage is supported by our data. individualized nutritional counseling should be attempted before implementing invasive nutritional intervention programs.(AJDC. 1989;143:458-464) SN - 0002-922X M3 - doi: 10.1001/archpedi.1989.02150160084017 UR - http://dx.doi.org/10.1001/archpedi.1989.02150160084017 ER -