TY  - JOUR
T1  - PRune belly syndrome
AU  - WALBAUM R
Y1  - 1979/03/01
N1  - 10.1001/archpedi.1979.02130030108024
JO  - American Journal of Diseases of Children
SP  - 332
EP  - 332
VL  - 133
IS  - 3
N2  - Sir.—In their report in the March 1978 issue of the Journal (132:316-317, 1978) of a patient with prune belly syndrome, Weber et al mentioned congenital cystic adenomatoid malformation of the lung as a previously undescribed accompaniment of this condition.In 1970, I saw a typical case of prune belly syndrome with polycystic malformation of the lower lobe of the right lung in a 2-month-old girl. The IVP was normal.Microscopic examination of the surgically removed right lower lobe disclosed multiple cavities lined by stratified cylindrical ciliated epithelium, resting on a loose collagenous chorion with scarce muscular fibers and rare dystrophic cartilaginous islets. Necrotic material, mucus, and polymorphonuclear leukocytes filled these cavities. A few atrophic alveoli were visible.This case was published (much too briefly!) in the French Pediatric Society's journal.1
SN  - 0002-922X
M3  - doi: 10.1001/archpedi.1979.02130030108024
UR  - http://dx.doi.org/10.1001/archpedi.1979.02130030108024
ER  -