RT Journal
A1 Schidlow DV, Panitch HB, Zaeri N, Zenel J, Alpert BE
T1 PUrpuric rashes in cystic fibrosis
JF American Journal of Diseases of Children
JO American Journal of Diseases of Children
YR 1989
FD September 1
VO 143
IS 9
SP 1030
OP 1032
DO 10.1001/archpedi.1989.02150210056018
UL http://dx.doi.org/10.1001/archpedi.1989.02150210056018
AB • Sixteen patients with cystic fibrosis experienced vasculitic rashes of the lower extremities that resembled hypergammaglobulinemic purpura. The rashes were associated with increased serum gammaglobulin G levels and rather severe lung disease. The rashes are probably the expression of chronic lung infection and high antigenic load in these patients. Their appearance was associated, in most cases, with poor long-term survival.(AJDC. 1989;143:1030-1032)