RT Journal
A1 Lipsitz PJ, Suser F, Weinberg S, Valderrama E
T1 COngenital unilateral ichthyosis in a newborn
JF American Journal of Diseases of Children
JO American Journal of Diseases of Children
YR 1979
FD January 1
VO 133
IS 1
SP 76
OP 78
DO 10.1001/archpedi.1979.02130010082016
UL http://dx.doi.org/10.1001/archpedi.1979.02130010082016
AB • Ichthyosiform erythroderma is a rare phenomenon occurring in about 1/300,000 live births. Congenital unilateral ichthyosis, described in this case report, is a clinical variant of ichthyosis. Only five previous cases have been reported. In the patient described in this report, superimposed infection of the affected skin developed. Her immunologic system was intact. She manifested failure to thrive, in spite of an adequate caloric intake, and markedly delayed psychomotor development. This patient also demonstrated absorption from the affected dermis of topically applied urea hydrophilic base ointment. She died before her first birthday.(Am J Dis Child 133:76-78, 1979)