0
Article |

Pathological Case of the Month FREE

V. Rehan, DCh(Lond), MD, MRCP, MRCPI; S. Phillips, MD; C. Fajardo, MD; M. M. K. Seshia, MB, ChB, FRCP(Edin)
Arch Pediatr Adolesc Med. 1997;151(11):1163-1164. doi:10.1001/archpedi.1997.02170480093016.
Text Size: A A A
Published online

THIS INFANT was born at 40 weeks' gestation to a 29-year-old gravida 2, para 0 white woman by vacuum delivery. Birth weight was 3770 g; crown-heel length, 56 cm; head circumference, 35.5 cm. Apgar scores were 7 and 7 at 1 and 5 minutes, respectively. Initial resuscitation included oropharyngeal suctioning and oxygen supplementation by face mask. Respiratory difficulty was soon noted. Ambient oxygen concentration was increased without benefit. At 1½ hours of age, he underwent intubation and ventilation. A chest radiograph showed bilateral pneumothoraces (Figure 1) that were drained through indwelling chest tubes with immediate improvement in oxygen saturation from 72% to 100%. Complete blood cell count, serum electrolyte level, and blood glucose level were normal. Arterial blood gas measurement showed pH, 7.45; PaO2, 73 mm Hg; PaCO2, 24 mm Hg; and bicarbonate, 17 mmol/L. Ventilatory rate ranged between 22 and 40/min; peak inspiratory pressure between 26 and

REFERENCES

Janney C, Askin F, Kuhn C III.  Congenital alveolar capillary dysplasia: an unusual cause of respiratory distress in the newborn . Am J Clin Pathol . 1981;;76: 722-727.
Boggs S, Harris MC, Hoffman DJ, et al.  Misalignment of pulmonary veins with capillary dysplasia: affected siblings and variable phenotypic expression . J Pediatr . 1994;;124:125-128.
Cullinane C, Cox P, Silver M.  Persistent pulmonary hypertension of the newborn due to alveolar capillary dysplasia . Pediatr Pathol . 1992;;12:499-514.
Cater G, Thibeault D, Beatty E Jr, Kilbride H, Huntrakoon M.  Misalignment of lung vessels and alveolar capillary dysplasia: a cause of persistent pulmonary hypertension . J Pediatr . 1989;;114:293-300.
Newman B, Yunis E.  Primary alveolar capillary dysplasia . Pediatr Radiol . 1990;; 21:20-22.
Steinhorn RH, Cox PN, Fineman JR, Zwass MC, Morin FC III.  Inhaled nitric oxide enhances oxygenation but not survival in infants with alveolar capillary dysplasia . J Pediatr . 1997;;130:417-422.

Figures

Tables

Interactive Graphics

Video

Country-Specific Mortality and Growth Failure in Infancy and Yound Children and Association With Material Stature

Use interactive graphics and maps to view and sort country-specific infant and early dhildhood mortality and growth failure data and their association with maternal

References

Janney C, Askin F, Kuhn C III.  Congenital alveolar capillary dysplasia: an unusual cause of respiratory distress in the newborn . Am J Clin Pathol . 1981;;76: 722-727.
Boggs S, Harris MC, Hoffman DJ, et al.  Misalignment of pulmonary veins with capillary dysplasia: affected siblings and variable phenotypic expression . J Pediatr . 1994;;124:125-128.
Cullinane C, Cox P, Silver M.  Persistent pulmonary hypertension of the newborn due to alveolar capillary dysplasia . Pediatr Pathol . 1992;;12:499-514.
Cater G, Thibeault D, Beatty E Jr, Kilbride H, Huntrakoon M.  Misalignment of lung vessels and alveolar capillary dysplasia: a cause of persistent pulmonary hypertension . J Pediatr . 1989;;114:293-300.
Newman B, Yunis E.  Primary alveolar capillary dysplasia . Pediatr Radiol . 1990;; 21:20-22.
Steinhorn RH, Cox PN, Fineman JR, Zwass MC, Morin FC III.  Inhaled nitric oxide enhances oxygenation but not survival in infants with alveolar capillary dysplasia . J Pediatr . 1997;;130:417-422.

Correspondence

CME
Accreditation Information
The American Medical Association is accredited by the Accreditation Council for Continuing Medical Education to provide continuing medical education for physicians. The AMA designates this journal-based CME activity for a maximum of 1 AMA PRA Category 1 CreditTM per course. Physicians should claim only the credit commensurate with the extent of their participation in the activity. Physicians who complete the CME course and score at least 80% correct on the quiz are eligible for AMA PRA Category 1 CreditTM.
Note: You must get at least of the answers correct to pass this quiz.
You have not filled in all the answers to complete this quiz
The following questions were not answered:
Sorry, you have unsuccessfully completed this CME quiz with a score of
The following questions were not answered correctly:
Commitment to Change (optional):
Indicate what change(s) you will implement in your practice, if any, based on this CME course.
Your quiz results:
The filled radio buttons indicate your responses. The preferred responses are highlighted
For CME Course: A Proposed Model for Initial Assessment and Management of Acute Heart Failure Syndromes
Indicate what changes(s) you will implement in your practice, if any, based on this CME course.
NOTE:
Citing articles are presented as examples only. In non-demo SCM6 implementation, integration with CrossRef’s “Cited By” API will populate this tab (http://www.crossref.org/citedby.html).
Submit a Comment

Some tools below are only available to our subscribers or users with an online account.

Related Content

Customize your page view by dragging & repositioning the boxes below.