A 3½-year-old child from Brazil presented with leukocoria of the left eye. Esotropia was the first manifestation of an eye problem and was noted 18 months before presentation. A computed tomographic scan of the eyes and orbits was performed.
Denouement and Discussion
Retinal Telangiectasia (Coats' Disease)
Manifestations
Coats' disease is a rare, chronic, progressive retinal disorder characterized by vascular changes and exudation. The vascular abnormalities include telangiectasia, microaneurysms, and dilated, tortuous vessels. The exudation is a result of leakage of plasma and cellular elements from the vascular abnormalities and may affect both retinal and subretinal tissues. The most striking funduscopic findings in Coats' disease are the yellowish exudates that form a circinate patternA 3½-year-old child from Brazil presented with leukocoria of the left eye. Esotropia was the first manifestation of an eye problem and was noted 18 months before presentation. A computed tomographic scan of the eyes and orbits was performed.
Denouement and Discussion
Retinal Telangiectasia (Coats' Disease)
Manifestations
Coats' disease is a rare, chronic, progressive retinal disorder characterized by vascular changes and exudation. The vascular abnormalities include telangiectasia, microaneurysms, and dilated, tortuous vessels. The exudation is a result of leakage of plasma and cellular elements from the vascular abnormalities and may affect both retinal and subretinal tissues. The most striking funduscopic findings in Coats' disease are the yellowish exudates that form a circinate pattern around the abnormal retinal vessels.
Origin
Coats' disease is sporadic in occurrence and of unknown origin. It is usually unilateral, although rare bilateral cases have been described.1 Two thirds of the reported cases occur in males, and