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February 1990, Vol 144, No. 2 >
Article | February 1990

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Sami B. Elhassani, MD; Tally Lerman-Sagie, MD; Marc Mimouni, MD; A. Metzker, MD; Murray Feingold, MD
[+] Author Affiliations

Accepted for publication June 6, 1989.

Reprint requests to the National Birth Defects Center, Franciscan Children's Hospital, 30 Warren St, Brighton, MA 02135 (Dr Feingold).


Am J Dis Child. 1990;144(2):207-208. doi:10.1001/archpedi.1990.02150260087035.
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References
Comments

The statements listed below are best associated with which of the above figures:

  • (a) This condition is not associated with a tumor, and because it is difficult to treat, it may require amputation.

  • (b) An asymptomatic upper abdominal mass is present.

  • (c) Deep venous abnormalities are associated with this syndrome.

  • (d) In this condition, hemiatrophy, and not hemihypertrophy, is present.

Denouement and Discussion  (a) Proximal femoral focal deficiency (Fig 3) is a congenital defect of unknown cause, usually consisting of a shortening of the proximal portion of the femur, with or without involvement of the pelvic bones. The severity of the condition depends on the presence or absence of the femoral head and the acetabulum. Treatment is directed toward stabilizing the hip. Correction of the leg length discrepancy may require a Syme's amputation above the knee and then fitting with a prosthesis.(b) Wilms' tumor, one of the most common

REFERENCES

1 +
Baskerville PA, Ackroid JS, Browse NL.  The etiology of Klippel-Trenaunay syndrome . Ann Surg . 1985;;202:624-627.
2 +
Baskerville PA, Ackroid JS, Thomas LM, et al.  The Klippel-Trenaunay syndrome: clinical, radiological, and hemodynamic features and management . Br J Surg . 1985;;72:232-236.
3 +
Kobrinsky NL, Talgoy M, Shuckett B, et al.  Wilms tumor . Ped Ann . 1988;;17:238-250.
4 +
Rogers M, Poyzer KG.  Cutis marmorata telangiectasia congenita . Arch Dermatol . 1982;;118:895-899.
5 +
Powell ST, Su WPD.  Cutis marmorata telangiectatica congenita: report of nine cases and review of the literature . Cutis . 1984;;34:305-312.
6 +
Kalamchi A, Cowell HR, Kim KI.  Congenital deficiency of the femur . J Pediatr Orthop . 1985;;5:129-134.

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Country-Specific Mortality and Growth Failure in Infancy and Yound Children and Association With Material Stature

Use interactive graphics and maps to view and sort country-specific infant and early dhildhood mortality and growth failure data and their association with maternal

References

1 +
Baskerville PA, Ackroid JS, Browse NL.  The etiology of Klippel-Trenaunay syndrome . Ann Surg . 1985;;202:624-627.
2 +
Baskerville PA, Ackroid JS, Thomas LM, et al.  The Klippel-Trenaunay syndrome: clinical, radiological, and hemodynamic features and management . Br J Surg . 1985;;72:232-236.
3 +
Kobrinsky NL, Talgoy M, Shuckett B, et al.  Wilms tumor . Ped Ann . 1988;;17:238-250.
4 +
Rogers M, Poyzer KG.  Cutis marmorata telangiectasia congenita . Arch Dermatol . 1982;;118:895-899.
5 +
Powell ST, Su WPD.  Cutis marmorata telangiectatica congenita: report of nine cases and review of the literature . Cutis . 1984;;34:305-312.
6 +
Kalamchi A, Cowell HR, Kim KI.  Congenital deficiency of the femur . J Pediatr Orthop . 1985;;5:129-134.

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