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July 1988, Vol 142, No. 7 >
Article | July 1988

Radiological Case of the Month FREE

Shahid N. Khan, MB, BS; Karen G. Hufnagle, MD, PhD; Beverly P. Wood, MD
[+] Author Affiliations

Accepted for publication by Lionel W. Young, MD, former section editor, Nov 17, 1987.

Reprint requests to Department of Radiology, Children's Hospital Medical Center of Akron, 281 Locust St, Akron, OH 44308 (Dr L. W. Young).


Am J Dis Child. 1988;142(7):781-782. doi:10.1001/archpedi.1988.02150070095034.
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A full-term, 2.76-kg female newborn infant in respiratory distress was delivered by emergency cesarean section from her 27-year-old primigravida mother. The prenatal period was uneventful, the baby's father had been in good health, and the family history yielded no information of concern. The infant had multiple, nodular, purplish skin lesions approximately 2 to 5 mm in diameter on her trunk and limbs. In addition, multiple smooth, mobile, and firm subcutaneous nodules approximately 0.5 to 1 cm in diameter were palpable in the limbs. Her face was not dysmorphic. On admission, her fundi were normal, but at follow-up examinations, hypopigmented retinal lesions were observed. Moderate subcostal retractions were present, and a grade 2/6 murmur was audible along the left sternal border. Her liver was palpable 3 to 4 cm below the right costal margin and was firm and nodular. The spleen also was moderately enlarged and firm. The infant appeared neurologically

REFERENCES

1 +
Stout AP:  Juvenile fibromatoses . Cancer 1954;;7:953-978.
2 +
Chung EB, Enzinger FM:  Infantile myofibromatosis . Cancer 1981;;48:1807-1818.
3 +
Brill PW, Yandow DR, Langer LO, et al:  Congenital generalized fibromatosis: Case report and literature review . Pediatr Radiol 1982;;12:269-278.
4 +
Baer JW, Radkowski MA:  Congenital multiple fibromatosis: A case report with review of the world litrature . AJR 1973;;118:200-205.
5 +
Morettin LB, Mueller E, Schreiber M:  Generalized hamartomatosis (congenital generalized fibromatosis) . AJR 1972;;114:722-734.
6 +
Enzinger FM, Smith BH:  Hemangiopericytoma: An analysis of 106 cases . Hum Pathol 1976;;7:61-82.
7 +
Baird PA, Worth AJ:  Congenital generalized fibromatosis: An autosomal recessive condition? Clin Genet 1976;;9:488-494.
8 +
Jennings TA, Duray PH, Collins FS, et al:  Infantile myofibromatosis: Evidence for an autosomal-dominant disorder . Am J Surg Pathol 1984;;8:529-538.
9 +
Mackenzie DH: The Differential Diagnosis of Fibroblastic Disorders . Boston, Blackwell Scientific Publication Inc, 1970;.
10 +
Teng P, Warden MJ, Cohn WL:  Congenital generalized fibromatosis (renal and skeletal) with complete spontaneous regression . J Pediatr 1963;;62:748-753.

Figures

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Country-Specific Mortality and Growth Failure in Infancy and Yound Children and Association With Material Stature

Use interactive graphics and maps to view and sort country-specific infant and early dhildhood mortality and growth failure data and their association with maternal

References

1 +
Stout AP:  Juvenile fibromatoses . Cancer 1954;;7:953-978.
2 +
Chung EB, Enzinger FM:  Infantile myofibromatosis . Cancer 1981;;48:1807-1818.
3 +
Brill PW, Yandow DR, Langer LO, et al:  Congenital generalized fibromatosis: Case report and literature review . Pediatr Radiol 1982;;12:269-278.
4 +
Baer JW, Radkowski MA:  Congenital multiple fibromatosis: A case report with review of the world litrature . AJR 1973;;118:200-205.
5 +
Morettin LB, Mueller E, Schreiber M:  Generalized hamartomatosis (congenital generalized fibromatosis) . AJR 1972;;114:722-734.
6 +
Enzinger FM, Smith BH:  Hemangiopericytoma: An analysis of 106 cases . Hum Pathol 1976;;7:61-82.
7 +
Baird PA, Worth AJ:  Congenital generalized fibromatosis: An autosomal recessive condition? Clin Genet 1976;;9:488-494.
8 +
Jennings TA, Duray PH, Collins FS, et al:  Infantile myofibromatosis: Evidence for an autosomal-dominant disorder . Am J Surg Pathol 1984;;8:529-538.
9 +
Mackenzie DH: The Differential Diagnosis of Fibroblastic Disorders . Boston, Blackwell Scientific Publication Inc, 1970;.
10 +
Teng P, Warden MJ, Cohn WL:  Congenital generalized fibromatosis (renal and skeletal) with complete spontaneous regression . J Pediatr 1963;;62:748-753.

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