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December 1985, Vol 139, No. 12 >
Article | December 1985

Aplasia Cutis Congenita and Lymphangiectasia FREE

WALLACE A. GLEASON, MD
Am J Dis Child. 1985;139(12):1178. doi:10.1001/archpedi.1985.02140140012004.
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Sir.—I noted with interest the report by Bronspiegel et al of the association between aplasia cutis congenita and intestinal lymphangiectasia.1 Table 2 in that article described clinical phenomena associated with intestinal lymphangiectasia and included a claimed association between Turner's syndrome and intestinal lymphangiectasia. The article cited to support that association was given as "Benson PF: Turner syndrome with intestinal lymphangiectasia. Arch Dis Child 1965;40:27."

An article by Benson and his associates entitled "Lymphangiography and Chromosome Studies in Females with Lymphoedema and Possible Ovarian Dysgenesis" appeared on page 27 of volume 40 of the Archives of Diseases in Childhood in 1965.2 This report contained details of lymphangiography in seven cases of Turner's syndrome, but nowhere did it mention intestinal lymphangiectasia.

Bronspiegel et al correctly pointed out the association between Noonan syndrome and intestinal lymphangiectasia. Considering the similarity between Noonan's and Turner's syndromes, the finding of intestinal lymphangiectasia in a patient with

REFERENCES

1 +
Bronspiegel N, Zelnick N, Rabinowitz H, et al:  Aplasia cutis congenita and intestinal lymphangiectasia: An unusual association . AJDC 1985;;139:509-513.
2 +
Benson PF, Gough MH, Polani PE:  Lymphangiography and chromosome studies in females with lymphoedema and possible ovarian dysgenesis . Arch Dis Child 1965;;40:27-32.
3 +
Gleason WA, Roodman ST, Laks H:  Proteinlosing enteropathy and intestinal lymphangiectasia after superior vena cava–right pulmonary artery (Glenn) shunt . J Thorac Cardiovasc Surg 1979;;77:843-846.
4 +
Vardy PA, Lebenthal E, Schwachman H:  Intestinal lymphangiectasia: A reappraisal . Pediatrics 1975;;55:842-851.
5 +
Haddad HH, Wilkins L:  Congenital anomalies associated with gonadal aplasia . Pediatrics 1959;;23:885-902.

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Country-Specific Mortality and Growth Failure in Infancy and Yound Children and Association With Material Stature

Use interactive graphics and maps to view and sort country-specific infant and early dhildhood mortality and growth failure data and their association with maternal

References

1 +
Bronspiegel N, Zelnick N, Rabinowitz H, et al:  Aplasia cutis congenita and intestinal lymphangiectasia: An unusual association . AJDC 1985;;139:509-513.
2 +
Benson PF, Gough MH, Polani PE:  Lymphangiography and chromosome studies in females with lymphoedema and possible ovarian dysgenesis . Arch Dis Child 1965;;40:27-32.
3 +
Gleason WA, Roodman ST, Laks H:  Proteinlosing enteropathy and intestinal lymphangiectasia after superior vena cava–right pulmonary artery (Glenn) shunt . J Thorac Cardiovasc Surg 1979;;77:843-846.
4 +
Vardy PA, Lebenthal E, Schwachman H:  Intestinal lymphangiectasia: A reappraisal . Pediatrics 1975;;55:842-851.
5 +
Haddad HH, Wilkins L:  Congenital anomalies associated with gonadal aplasia . Pediatrics 1959;;23:885-902.

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