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Radiological Case of the Month FREE

Michael A. Portman, MD; Thomas W. Riggs, MD; Ronald B. Port, MD; Lionel W. Young, MD
[+] Author Affiliations

Reprint requests to Department of Radiology, Children's Hospital of Pittsburgh, 125 DeSoto St, Pittsburgh, PA 15213 (Dr L. W. Young).


Am J Dis Child. 1984;138(7):697-698. doi:10.1001/archpedi.1984.02140450079024.
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A 3,170-g term male infant was delivered via cesarean section because of failure of labor to progress. Pregnancy had been complicated by polyhydramnios, which was diagnosed by ultrasound. The infant had Apgar scores of 4 and 7 at one and five minutes, respectively, and cyanosis and respiratory distress developed shortly after delivery. Breath sounds were decreased over the left hemithorax, and the heart sounds and cardiac impulse were maximal over the right hemithorax. The second heart sound was loud and single. A grade 3/6 harsh systolic murmur alternated with a rough decrescendo diastolic murmur along the right sternal border to give a "to-and-fro" auscultatory sound.

After endotracheal intubation, a chest roentgenogram (Fig 1) was obtained and arterial blood gas determinations in 100% inspired oxygen demonstrated the following values: pH, 7.32; Pco2, 40 mm Hg; Po2, 38 mm Hg; and base excess, 5.3 mEq. The infant was

REFERENCES

Lakier JB, Stanger P, Heymann MA, et al:  Tetralogy of Fallot with absent pulmonary valve: Natural history and hemodynamic considerations . Circulation 1974;;50:167-175.
Emmanouilides GC, Thanopoulos B, Siassi B, et al:  'Agenesis' of ductus arteriosus associated with the syndrome of tetralogy of Fallot and absent pulmonary valve . Am J Cardiol 1976;;37: 403-409.
Borg SA, Young LW, Roghair CD:  Congenital avalvular pulmonary artery and infantile lobar emphysema: A diagnostic correlation . AJR 1975;;125:412-421.
Rabinovitch M, Grady S, David I, et al:  Compression of intrapulmonary bronchi by abnormally branching pulmonary arteries associated with absent pulmonary valves . Am J Cardiol 1982;;50:804-813.
Pernot C, Hoeffel JC, Henry M, et al:  Radiological patterns of congenital absence of the pulmonary valve in infants . Radiology 1972;;102: 619-622.
Ilbawi MN, Idriss FS, Muster AJ, et al:  Tetralogy of Fallot with absent pulmonary valve: Should valve insertion be part of the intracardiac repair? J Thorac Cardiovasc Surg 1981;;81: 906-915.
Pinsky WW, Nihill MR, Mullins CE, et al:  The absent pulmonary valve syndrome: Considerations of management . Circulation 1978;;57: 159-161.

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Country-Specific Mortality and Growth Failure in Infancy and Yound Children and Association With Material Stature

Use interactive graphics and maps to view and sort country-specific infant and early dhildhood mortality and growth failure data and their association with maternal

References

Lakier JB, Stanger P, Heymann MA, et al:  Tetralogy of Fallot with absent pulmonary valve: Natural history and hemodynamic considerations . Circulation 1974;;50:167-175.
Emmanouilides GC, Thanopoulos B, Siassi B, et al:  'Agenesis' of ductus arteriosus associated with the syndrome of tetralogy of Fallot and absent pulmonary valve . Am J Cardiol 1976;;37: 403-409.
Borg SA, Young LW, Roghair CD:  Congenital avalvular pulmonary artery and infantile lobar emphysema: A diagnostic correlation . AJR 1975;;125:412-421.
Rabinovitch M, Grady S, David I, et al:  Compression of intrapulmonary bronchi by abnormally branching pulmonary arteries associated with absent pulmonary valves . Am J Cardiol 1982;;50:804-813.
Pernot C, Hoeffel JC, Henry M, et al:  Radiological patterns of congenital absence of the pulmonary valve in infants . Radiology 1972;;102: 619-622.
Ilbawi MN, Idriss FS, Muster AJ, et al:  Tetralogy of Fallot with absent pulmonary valve: Should valve insertion be part of the intracardiac repair? J Thorac Cardiovasc Surg 1981;;81: 906-915.
Pinsky WW, Nihill MR, Mullins CE, et al:  The absent pulmonary valve syndrome: Considerations of management . Circulation 1978;;57: 159-161.

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