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Congenital Middle Ear Cholesteatoma FREE

RICHARD H. SCHWARTZ, MD; KENNETH M. GRUNDFAST, MD; WILLIAM J. McAVENEY, MD; MARCO A. MERIDA, MD; BRUCE FELDMAN, MD
Am J Dis Child. 1983;137(5):501-502. doi:10.1001/archpedi.1983.02140310079022.
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A congenital aural cholesteatoma is a cystic epithelial remnant of embryonal origin found medial to the intact tympanic membrane. This entity may be identified in young children who have not had perforated eardrums and who have had no history of otitis media. The keratoma may be located within the temporal bone, in the region of the petrous apex, in the middle ear cleft (mesotympanic cholesteatoma), or enclosed within the layers of the tympanic membrane (intramembranous cholesteatoma). These rare pseudotumors can simulate persistent otitis media with effusion and, if unrecognized, they can grow, become infected, and in time cause extensive destruction of the middle ear ossicles and mastoid. We describe two infants who had congenital mesotympanic cholesteatoma during routine well-baby examinations. The initial clinical impression in both cases was that the entity was loculated exudate from acute otitis media with effusion.

Report of Cases.—Case 1.—At the three-month routine checkup

REFERENCES

Curtis AW:  Congenital middle ear cholesteatoma: Two unusual cases and a review of the literature . Laryngoscope 1981;;89:1159-1165.
House HP:  An apparent primary cholesteatoma: Case report . Laryngoscope 1953;;63:612-613.
Laff HI:  Two cases of primary latent cholesteatoma diagnosed and treated by tympanoplasty . Trans Am Laryngol Rhinol Otol Soc 1959;;69:369-380.
Derlacki EL, Harrison WH, Clemis JD:  Congenital cholesteatoma of the middle ear and mastoid: A second report presenting seven additional cases . Laryngoscope 1968;;78:1050-1078.
Derlacki EL, Clemis JD:  Congenital cholesteatoma of the middle ear and mastoid . Ann Otol Rhinol Laryngol 1965;;74:706-727.
Derlacki EL:  Congenital cholesteatoma of the middle ear and mastoid: A third report . Arch Otolaryngol 1973;;97:177-182.
Peron DL, Schuknecht HF:  Congenital cholesteatoma with other anomalies . Arch Otolaryngol 1975;;101:498-505.
House J, Sheehy J:  Cholesteatoma with intact tympanic membrane: A report of 41 cases . Laryngoscope 1980;;90:70-75.
Cross JP:  Otomastoid cholesteatomas with intact eardrum . Laryngoscope 1981;;91:1145-1149.
Smith R, Moran WB:  Tympanic membrane keratoma (cholesteatoma) in children with no prior otologic surgery . Laryngoscope 1977;;87: 237-245.
Sobol SM, Reichert TJ, Jaw KD, et al:  Intramembranous and mesotympanic cholesteatomas associated with intact tympanic membranes in children . Ann Otol Rhinol Laryngol 1980;;89:312-317.
Cruveilhier J: Anatomic pathologique du corp humain . Paris, JB Balliere, 1829;, vol 1, p 341.
Fernandez C, Lindsay JR, Moskowitz M:  Some observations on the pathogenesis of middle ear cholesteatoma . Arch Otolaryngol 1959;;69: 537-546.
Holmes EM:  A review of 303 cases of cholesteatoma . Ann Otol Rhinol Laryngol 1938;; 47:135-143.
Ruedi L:  Pathogenesis and treatment of cholesteatoma in chronic suppuration of the temporal bone . Ann Otol Rhinol Laryngol 1957;;66: 283-305.

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References

Curtis AW:  Congenital middle ear cholesteatoma: Two unusual cases and a review of the literature . Laryngoscope 1981;;89:1159-1165.
House HP:  An apparent primary cholesteatoma: Case report . Laryngoscope 1953;;63:612-613.
Laff HI:  Two cases of primary latent cholesteatoma diagnosed and treated by tympanoplasty . Trans Am Laryngol Rhinol Otol Soc 1959;;69:369-380.
Derlacki EL, Harrison WH, Clemis JD:  Congenital cholesteatoma of the middle ear and mastoid: A second report presenting seven additional cases . Laryngoscope 1968;;78:1050-1078.
Derlacki EL, Clemis JD:  Congenital cholesteatoma of the middle ear and mastoid . Ann Otol Rhinol Laryngol 1965;;74:706-727.
Derlacki EL:  Congenital cholesteatoma of the middle ear and mastoid: A third report . Arch Otolaryngol 1973;;97:177-182.
Peron DL, Schuknecht HF:  Congenital cholesteatoma with other anomalies . Arch Otolaryngol 1975;;101:498-505.
House J, Sheehy J:  Cholesteatoma with intact tympanic membrane: A report of 41 cases . Laryngoscope 1980;;90:70-75.
Cross JP:  Otomastoid cholesteatomas with intact eardrum . Laryngoscope 1981;;91:1145-1149.
Smith R, Moran WB:  Tympanic membrane keratoma (cholesteatoma) in children with no prior otologic surgery . Laryngoscope 1977;;87: 237-245.
Sobol SM, Reichert TJ, Jaw KD, et al:  Intramembranous and mesotympanic cholesteatomas associated with intact tympanic membranes in children . Ann Otol Rhinol Laryngol 1980;;89:312-317.
Cruveilhier J: Anatomic pathologique du corp humain . Paris, JB Balliere, 1829;, vol 1, p 341.
Fernandez C, Lindsay JR, Moskowitz M:  Some observations on the pathogenesis of middle ear cholesteatoma . Arch Otolaryngol 1959;;69: 537-546.
Holmes EM:  A review of 303 cases of cholesteatoma . Ann Otol Rhinol Laryngol 1938;; 47:135-143.
Ruedi L:  Pathogenesis and treatment of cholesteatoma in chronic suppuration of the temporal bone . Ann Otol Rhinol Laryngol 1957;;66: 283-305.

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