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February 1983, Vol 137, No. 2 >
Article | February 1983

Hydrocephalus and Shunt Placement FREE

JOHN VAN AERDE, MD; ALASTAIR CAMPBELL, MD, BS, MRCP
Am J Dis Child. 1983;137(2):187-188. doi:10.1001/archpedi.1983.02140280079029.
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Sir.—In their article "Acute Hydrocephalus in Hurler's Syndrome," Shinnar et al described two patients who were successfully treated by a venticuloperitoneal shunt (Journal 1982; 136:556-557). Although the association of mucopolysaccharidosis (MPS) with hydrocephalus is known, shunt placement has been performed very seldom. Three years ago, we treated a patient with Hunter's syndrome in the same manner with a good result.1

Report of a Case.—A boy suffered from the mild variety of Hunter's syndrome (MPS II-B) associated with moderate mitral regurgitation. His head circumference was always enlarged, but his intellectual development was normal. At the age of 19 years, he was admitted with bacterial endocarditis. During treatment, he complained of persisting headache and blurred vision. A computed tomographic (CT) scan showed severe hydrocephalus with dilation of all ventricles. A scintiscan, after lumbar injection of a tracer dose of technetium diethyltriaminepenta-acetic acid, showed a communicating hydrocephalus characterized by ventricular

REFERENCES

1 +
Van Aerde J, Plets C, Van Der Hauwaert L:  Hydrocephalus in Hunter syndrome . Acta Paediatr Belg 1981;;34:93-96.
2 +
Ford FR:  Gargoylism , in Diseases of the Nervous System in Infancy , Childhood and Adolescence, ed 6. Springfield, Ill, Charles C Thomas Publisher, 1973;, pp 905-910.
3 +
Fowler GW, Sukoff M, Hamilton A, et al:  Communicating hydrocephalus in children with genetic inborn errors of metabolism . Childs Brain 1975;;1:251-254.
4 +
Menkes JA:  The mucopolysaccharidoses , in Textbook of Child Neurology , ed 2. Philadelphia, Lea & Febiger, 1980;, pp 40-48.
5 +
Yatziv S, Epstein CJ:  Hunter syndrome presenting as macrocephaly and hydrocephalus . J Med Genet 1977;;14:445-447.
6 +
McKusick VA:  The mucopolysaccharidoses , in Heritable Disorders of Connective Tissue . St Louis, CV Mosby Co, 1972;, pp 521-686.
7 +
Tew B, Laurence KM:  The effect of hydrocephalus on intelligence, visual perception, and school attainment . Dev Med Child Neurol 1975;;17:129-134.
8 +
Yatziv S, Erickson RP, Epstein CJ:  Mild and severe Hunter syndrome (MPS II) within the same sibships . Clin Genet 1977;;11:319-326.

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Country-Specific Mortality and Growth Failure in Infancy and Yound Children and Association With Material Stature

Use interactive graphics and maps to view and sort country-specific infant and early dhildhood mortality and growth failure data and their association with maternal

References

1 +
Van Aerde J, Plets C, Van Der Hauwaert L:  Hydrocephalus in Hunter syndrome . Acta Paediatr Belg 1981;;34:93-96.
2 +
Ford FR:  Gargoylism , in Diseases of the Nervous System in Infancy , Childhood and Adolescence, ed 6. Springfield, Ill, Charles C Thomas Publisher, 1973;, pp 905-910.
3 +
Fowler GW, Sukoff M, Hamilton A, et al:  Communicating hydrocephalus in children with genetic inborn errors of metabolism . Childs Brain 1975;;1:251-254.
4 +
Menkes JA:  The mucopolysaccharidoses , in Textbook of Child Neurology , ed 2. Philadelphia, Lea & Febiger, 1980;, pp 40-48.
5 +
Yatziv S, Epstein CJ:  Hunter syndrome presenting as macrocephaly and hydrocephalus . J Med Genet 1977;;14:445-447.
6 +
McKusick VA:  The mucopolysaccharidoses , in Heritable Disorders of Connective Tissue . St Louis, CV Mosby Co, 1972;, pp 521-686.
7 +
Tew B, Laurence KM:  The effect of hydrocephalus on intelligence, visual perception, and school attainment . Dev Med Child Neurol 1975;;17:129-134.
8 +
Yatziv S, Erickson RP, Epstein CJ:  Mild and severe Hunter syndrome (MPS II) within the same sibships . Clin Genet 1977;;11:319-326.

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