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May 1978, Vol 132, No. 5 >
Article | May 1978

Association of Prune Belly Syndrome and Gastroschisis FREE

CRAIG WILLERT, MD; HOWARD COHEN, MD; YA-MEI T. Yu, MD; JOHN D. MADDEN, MD
Am J Dis Child. 1978;132(5):526-527. doi:10.1001/archpedi.1978.02120300086019.
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Prune belly and gastroschisis are syndromes that have been well described in the literature. Prune belly or the "triad syndrome" is composed of cryptorchidism, deficiency of the abdominal wall, musculature, and urinary tract abnormalities.1 -4 Gastroschisis is a congenital full-thickness cleft in the abdominal wall, usually to the right of a normally inserting umbilical cord, and evisceration through the defect with no overlying membrane.5 -8 There have been more than 200 cases of prune belly and greater than 120 cases of gastroschisis reported in the literature, but the two syndromes have not, to our knowledge, been described together in the same patient. This report describes a patient with both prune belly syndrome and gastroschisis.

Report of a Case.—This infant was delivered from a gravida 9, para 7, 37-year-old woman on June 23, 1976 in Chicago Osteopathic Hospital. Excessive maternal alcohol consumption was the only complication of pregnancy.

REFERENCES

1 +
Eagle JF, Barrett GS:  Congenital deficiency of abdominal musculature with associated genito-urinary abnormalities: A syndrome, report of nine cases . Pediatrics 6:721-736, 1950;.
2 +
Rogers LW, Ostrow PT:  The prune belly syndrome: Report of 20 cases and description of a lethal variant . J Pediatr 83:786-793, 1973;.
Link to Article
3 +
Ives EJ:  The abdominal muscle deficiency triad syndrome—Experience with ten cases . Birth Defects: Original Article Series , No. (4) , vol 10, pp 127-135, 1974;.
4 +
Cremin BJ:  The urinary tract anomalies associated with agenesis of the abdominal walls . Br J Radiol 44:767-772, 1971;.
Link to Article
5 +
Lewis JE, Kraeger RR, Danis RK:  Gastroschisis . Arch Surg 107:218-222, 1973;.
Link to Article
6 +
Gilbert MG, Mencia LF, Puranik SR, et al:  Management of gastroschisis and short bowel: Report of 17 cases . J Pediatr Surg 7:598-607, 1972;.
Link to Article
7 +
Mahour GH, Weitzman JJ, Rosenkrantz JG:  Omphalocele and gastroschisis . Ann Surg 177:478-482, 1973;.
Link to Article
8 +
Moore TC:  Gastroschisis with antenatal evisceration of intestines and urinary bladder . Ann Surg 158:263-269, 1963;.
Link to Article
9 +
Schuster SR:  A new method for the staged repair of omphalocele . Surg Gynecol Obstet 125:837, 1967;.

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References

1 +
Eagle JF, Barrett GS:  Congenital deficiency of abdominal musculature with associated genito-urinary abnormalities: A syndrome, report of nine cases . Pediatrics 6:721-736, 1950;.
2 +
Rogers LW, Ostrow PT:  The prune belly syndrome: Report of 20 cases and description of a lethal variant . J Pediatr 83:786-793, 1973;.
Link to Article
3 +
Ives EJ:  The abdominal muscle deficiency triad syndrome—Experience with ten cases . Birth Defects: Original Article Series , No. (4) , vol 10, pp 127-135, 1974;.
4 +
Cremin BJ:  The urinary tract anomalies associated with agenesis of the abdominal walls . Br J Radiol 44:767-772, 1971;.
Link to Article
5 +
Lewis JE, Kraeger RR, Danis RK:  Gastroschisis . Arch Surg 107:218-222, 1973;.
Link to Article
6 +
Gilbert MG, Mencia LF, Puranik SR, et al:  Management of gastroschisis and short bowel: Report of 17 cases . J Pediatr Surg 7:598-607, 1972;.
Link to Article
7 +
Mahour GH, Weitzman JJ, Rosenkrantz JG:  Omphalocele and gastroschisis . Ann Surg 177:478-482, 1973;.
Link to Article
8 +
Moore TC:  Gastroschisis with antenatal evisceration of intestines and urinary bladder . Ann Surg 158:263-269, 1963;.
Link to Article
9 +
Schuster SR:  A new method for the staged repair of omphalocele . Surg Gynecol Obstet 125:837, 1967;.

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