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Congenital Adrenal Hypoplasia and Hypogonadotropic Hypogonadism FREE

Michael P. Golden, MD; Barbara M. Lippe, MD; Solomon A. Kaplan, MD
[+] Author Affiliations

Reprint requests to Department of Pediatrics, UCLA School of Medicine, Los Angeles, CA 90024 (Dr Kaplan).


Am J Dis Child. 1977;131(10):1117-1118. doi:10.1001/archpedi.1977.02120230063010.
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• A 19-year-old male patient with congenital adrenal hypoplasia and elevated plasma adrenocorticotropic hormone level was found to have gonadotropin deficiency. Other hypothalamic-pituitary functions were normal. A possible relationship between hypothalamic-pituitary dysfunction and development of the cytomegalic form of congenital hypoplasia of the adrenals is suggested.

(Am J Dis Child 131:1117-1118, 1977)

REFERENCES

Kerenyi N:  Congenital adrenal hypoplasia . Arch Pathol 71:336-343, 1961;.
Sperling M, Wolfsen A, Fisher D:  Congenital adrenal hypoplasia: An isolated defect of organogenesis . J Pediatr 82:444-449, 1973;.
Link to Article
Weiss L, Mellinger R:  Congenital adrenal hypoplasia: An X-linked disease . J Med Genet 7:27-32, 1970;.
Link to Article
Brook C, Bambach M, Zachmann M, et al:  Familial congenital adrenal hypoplasia . Helv Paediatr Acta 28:277-282, 1973;.
Prader A, Zachmann M, Illig R:  Luteinizing hormone deficiency in hereditary congenital adrenal hypoplasia . J Pediatr 86:421-422, 1975;.
Link to Article
Zachmann M, Prader A, Kind HP, et al:  Testicular volume during adolescence: Cross sectional and longitudinal studies . Helv Paediatr Acta 29:61-72, 1974;.
Dickerman Z, Prager-Lewin R, Laron Z:  Response of plasma LH and FSH to synthetic LH-RH in children at various pubertal stages . Am J Dis Child 130:634-638, 1976;.
Baker W, Wise G, Mezger M:  Cytomegalic adrenal hypoplasia in a 4½-year-old boy . Am J Dis Child 114:180-185, 1967;.
Pakravan P, Kenny FM, Depp R, et al:  Familial congenital absence of adrenal glands: Evaluation of glucocorticoid, mineralocorticoid, and estrogen metabolism in the perinatal period . J Pediatr 84:74-78, 1974;.
Link to Article
Parker DC, Judd HL, Rossman LG, et al:  Pubertal sleep-wake patterns of episodic LH, FSH and Testosterone release in twin boys . J Clin Endocrinol Metab 40:1099-1109, 1975;.
Link to Article
Yoshimoto Y, Moridera K, Imura H:  Restoration of normal pituitary gonadotropin reserve by administration of luteinizing-hormone-releasing hormone in patients with hypogonadotropic hypogonadism . N Engl J Med 292:242-245, 1975;.
Link to Article

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References

Kerenyi N:  Congenital adrenal hypoplasia . Arch Pathol 71:336-343, 1961;.
Sperling M, Wolfsen A, Fisher D:  Congenital adrenal hypoplasia: An isolated defect of organogenesis . J Pediatr 82:444-449, 1973;.
Link to Article
Weiss L, Mellinger R:  Congenital adrenal hypoplasia: An X-linked disease . J Med Genet 7:27-32, 1970;.
Link to Article
Brook C, Bambach M, Zachmann M, et al:  Familial congenital adrenal hypoplasia . Helv Paediatr Acta 28:277-282, 1973;.
Prader A, Zachmann M, Illig R:  Luteinizing hormone deficiency in hereditary congenital adrenal hypoplasia . J Pediatr 86:421-422, 1975;.
Link to Article
Zachmann M, Prader A, Kind HP, et al:  Testicular volume during adolescence: Cross sectional and longitudinal studies . Helv Paediatr Acta 29:61-72, 1974;.
Dickerman Z, Prager-Lewin R, Laron Z:  Response of plasma LH and FSH to synthetic LH-RH in children at various pubertal stages . Am J Dis Child 130:634-638, 1976;.
Baker W, Wise G, Mezger M:  Cytomegalic adrenal hypoplasia in a 4½-year-old boy . Am J Dis Child 114:180-185, 1967;.
Pakravan P, Kenny FM, Depp R, et al:  Familial congenital absence of adrenal glands: Evaluation of glucocorticoid, mineralocorticoid, and estrogen metabolism in the perinatal period . J Pediatr 84:74-78, 1974;.
Link to Article
Parker DC, Judd HL, Rossman LG, et al:  Pubertal sleep-wake patterns of episodic LH, FSH and Testosterone release in twin boys . J Clin Endocrinol Metab 40:1099-1109, 1975;.
Link to Article
Yoshimoto Y, Moridera K, Imura H:  Restoration of normal pituitary gonadotropin reserve by administration of luteinizing-hormone-releasing hormone in patients with hypogonadotropic hypogonadism . N Engl J Med 292:242-245, 1975;.
Link to Article

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