0
Article |

Picture of the Month

Sydney S. Gellis, MD; Murray Feingold, MD; T. Allen Merritt, MD; Ronald Slaughter, MD
Am J Dis Child. 1977;131(9):1027-1028. doi:10.1001/archpedi.1977.02120220093016.
Text Size: A A A
Published online

Denouement and Discussion 

Cutis Marmorata Telangiectasia Congenita (Congenital Generalized Phlebectasia) 

Manifestations  A congenital pattern of prominent capillaries and veins is present and is manifested as a bluish-red, lace-like pattern over the trunk, limbs, and face of the neonate. These mottled areas easily blanch with slight pressure, and the overlying skin has a thin, parchment-like quality. Congenital glaucoma, patent ductus arteriosus, and mental retardation have also been reported.Skin biopsy of the involved areas shows dilated capillaries and veins, with occasional thin-walled sinusoids in both the dermis and subcutaneous tissue. Ectatic vessels confined only to the dermis have also been reported.Cutis marmorata telangiectasia congenita (CMTC) has been described with other vascular defects such as local varicosities, hemangiomatous malformations, and bone and soft tissue atrophy and hypertrophy. This has raised the possibility that CMTC is part of the spectrum of the Klippel-Trenaunay syndrome. However, in most of the cases, the disorder

Topics

Sign In to Access Full Content

Don't have Access?

Register and get free email Table of Contents alerts, saved searches, PowerPoint downloads, CME quizzes, and more

Subscribe for full-text access to content from 1998 forward and a host of useful features

Activate your current subscription (AMA members and current subscribers)

Purchase Online Access to this article for 24 hours

First Page Preview

View Large
/>
First page PDF preview

Figures

Tables

References

Correspondence

CME
Meets CME requirements for:
Browse CME for all U.S. States
Accreditation Information
The American Medical Association is accredited by the Accreditation Council for Continuing Medical Education to provide continuing medical education for physicians. The AMA designates this journal-based CME activity for a maximum of 1 AMA PRA Category 1 CreditTM per course. Physicians should claim only the credit commensurate with the extent of their participation in the activity. Physicians who complete the CME course and score at least 80% correct on the quiz are eligible for AMA PRA Category 1 CreditTM.
Note: You must get at least of the answers correct to pass this quiz.
You have not filled in all the answers to complete this quiz
The following questions were not answered:
Sorry, you have unsuccessfully completed this CME quiz with a score of
The following questions were not answered correctly:
Commitment to Change (optional):
Indicate what change(s) you will implement in your practice, if any, based on this CME course.
Your quiz results:
The filled radio buttons indicate your responses. The preferred responses are highlighted
For CME Course: A Proposed Model for Initial Assessment and Management of Acute Heart Failure Syndromes
Indicate what changes(s) you will implement in your practice, if any, based on this CME course.
NOTE:
Citing articles are presented as examples only. In non-demo SCM6 implementation, integration with CrossRef’s "Cited By" API will populate this tab (http://www.crossref.org/citedby.html).
Submit a Comment

Multimedia

Some tools below are only available to our subscribers or users with an online account.

Sign In to Access Full Content

Related Content

Customize your page view by dragging & repositioning the boxes below.

Jobs
brightcove.createExperiences();