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Prune-Belly Syndrome Associated With Potter (Renal Nonfunction) Syndrome FREE

Arun K. Pramanik, MD; Geoffrey Altshuler, MB, BS; Irwin J. Light, MD; James M. Sutherland, MD
[+] Author Affiliations

Reprint requests to University of Cincinnati, College of Medicine, 231 Bethesda Ave, Cincinnati, OH 45267 (Dr Light).


Am J Dis Child. 1977;131(6):672-674. doi:10.1001/archpedi.1977.02120190066013.
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• Three fatal cases of prune-belly syndrome were associated with nonrenal features of Potter syndrome. The abdominal muscle hypoplasia is thought to be a result of large kidneys compressing the developing abdominal musculature during a critical phase of fetal development. Thus, Potter syndrome and prune-belly syndrome may coexist when nonfunctioning large kidneys result in oligohydramnios. A teratogenic role of cytomegalovirus inclusion disease and other viruses is possible in the pathogenesis of these syndromes.

(Am J Dis Child 131:672-674, 1977)

REFERENCES

Parker RW:  Absence of abdominal muscles in an infant . Lancet 1:1252-1254, 1895;.
Adebonojo FO:  Dysplasia of the anterior abdominal musculature with multiple congenital anomalies, prune-belly or triad syndrome . J Natl Med Assoc 65:327-333, 1973;.
Rogers LW, Ostrow PT:  The prune-belly syndrome: Report of 20 cases and description of a lethal variant . J Pediatr 83:786-793, 1973;.
Link to Article
Thomas IT, Smith DW:  Oligohydramnios, cause of non-renal features of Potter's syndrome, including pulmonary hypoplasia . J Pediatr 84:811-814, 1974;.
Link to Article
Altshuler G, Russell P:  Human placental villitides: A review of chronic intrauterine infection . Curr Top Pathol 60:63-112, 1975;.
Osthanondh V, Potter EL:  Pathogenesis of polycystic kidney, type 4 due to urethral obstruction . Arch Pathol 77:510-513, 1964;.
Bain AD, Scott JS:  Renal agenesis and severe urinary tract dysplasia . Br Med J 1:841-846, 1960;.
Link to Article
Potter EL:  Oligohydramnios: Further comment . J Pediatr 84:931-932, 1974;.
Link to Article
Fitch N, Lachance RC:  The pathogenesis of Potter's syndrome of renal agenesis . Can Med Assoc J 107:653-656, 1972;.
Symmond DA, Driscoll SG:  Massive fetal ascites, urethral atresia and cytomegalic inclusion disease . Am J Dis Child 127:895-897, 1974;.
Benirschke K, Mendoza GR, Bazeley PL:  Placental and fetal manifestations of cytomegalovirus infection . Virchows Arch 16:121-139, 1974;.

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Country-Specific Mortality and Growth Failure in Infancy and Yound Children and Association With Material Stature

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References

Parker RW:  Absence of abdominal muscles in an infant . Lancet 1:1252-1254, 1895;.
Adebonojo FO:  Dysplasia of the anterior abdominal musculature with multiple congenital anomalies, prune-belly or triad syndrome . J Natl Med Assoc 65:327-333, 1973;.
Rogers LW, Ostrow PT:  The prune-belly syndrome: Report of 20 cases and description of a lethal variant . J Pediatr 83:786-793, 1973;.
Link to Article
Thomas IT, Smith DW:  Oligohydramnios, cause of non-renal features of Potter's syndrome, including pulmonary hypoplasia . J Pediatr 84:811-814, 1974;.
Link to Article
Altshuler G, Russell P:  Human placental villitides: A review of chronic intrauterine infection . Curr Top Pathol 60:63-112, 1975;.
Osthanondh V, Potter EL:  Pathogenesis of polycystic kidney, type 4 due to urethral obstruction . Arch Pathol 77:510-513, 1964;.
Bain AD, Scott JS:  Renal agenesis and severe urinary tract dysplasia . Br Med J 1:841-846, 1960;.
Link to Article
Potter EL:  Oligohydramnios: Further comment . J Pediatr 84:931-932, 1974;.
Link to Article
Fitch N, Lachance RC:  The pathogenesis of Potter's syndrome of renal agenesis . Can Med Assoc J 107:653-656, 1972;.
Symmond DA, Driscoll SG:  Massive fetal ascites, urethral atresia and cytomegalic inclusion disease . Am J Dis Child 127:895-897, 1974;.
Benirschke K, Mendoza GR, Bazeley PL:  Placental and fetal manifestations of cytomegalovirus infection . Virchows Arch 16:121-139, 1974;.

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