0
Article |

Hereditary Recurrent Brachial Neuropathy FREE

Noel Guillozet, MD; Robert D. Mercer, MD
[+] Author Affiliations

Received for publication Aug 24, 1972; accepted March 19, 1973.

Reprint requests to Southern Monterey County Medical Group, 210 Canal St, King City, CA 93930 (Dr. Guillozet).


Am J Dis Child. 1973;125(6):884-887. doi:10.1001/archpedi.1973.04160060082019.
Text Size: A A A
Published online

A 7-year-old boy with hereditary recurrent brachial neuropathy is described and the disease is traced through three generations. The disease is thought to be transmitted by an autosomal dominant gene. There is a wide spectrum of severity of attacks which have a tendency to recur at long intervals to appear during pregnancy or parturition. A troublesome but generally benign course can be predicted. There is no evidence at this time to believe that treatment other than supportive care has any real value.

REFERENCES

Dreschfeld J:  On some of the rarer forms of muscular atrophies . Brain 9:178-195, 1887;.
Ross J, Bury JS: On peripheral neuritis . London, 1893;.
Davies DM:  Recurrent peripheralnerve palsies in a family . Lancet 2:266-268, 1954;.
Ungley CC:  Recurrent polyneuritis in pregnancy and the puerperium affecting three members of a family . J Neurol Psychopathol 14:15-26, 1933;.
Taylor RA:  Heredofamilial mononeuritis multiplex with brachial predilection . Brain 83:113-137, 1960;.
Jacob JC, Andermann F, Robb JP:  Heredofamilial neuritis with brachial predilection . Neurology 11:1025-1033, 1961;.
Gardner JH, Maloney W:  Hereditary brachial and cranial neuritis genetically linked with ocular hypotelorism and syndactly . Neurology 18:278-281, 1968;.
Wyburn-Mason R:  Brachial neuritis occurring in epidemic form . Lancet 2:662-663, 1941;.
Spillane JD:  Localized neuritis of the shoulder girdle . Lancet 2:532-535, 1943;.
Parsonage MJ, Turner JWA:  Neuralgic amyotrophy: The shoulder-girdle syndrome . Lancet 1:973-978, 1948;.
Turner JWA, Parsonage JF:  Neuralgic amyotrophy (paralytic brachial neuritis) with reference to prognosis . Lancet 2:209-212, 1957;.
Magee KR, DeJong RN:  Paralytic brachial neuritis: Discussion of clinical features with review of 23 cases . JAMA 174:1258-1262, 1960;.
Evans HW:  Paralytic brachial neuritis: Report of a case . Lancet 83:251-252, 1963;.
Kennedy WR, Resch JA:  Paralytic brachial neuritis . Lancet 86:459-462, 1966;.
Dejerine J, Sottas J:  Sur la nevrite intestitielle, hypertrophique et progressive de l'enfance . Compt Rend Soc Biol 5:63-96, 1893;.
de Bruyn RS, Stern RO:  A case of the progressive hypertrophic polyneuritis of Dejerine and Sottas, with pathological examination . Brain 52:84-107, 1929;.
Fleming R:  Refsum's syndrome: An unusual hereditary neuropathy . Neurology 7:476-479, 1957;.
Austin JH:  Recurrent polyneuropathies and their corticosteroid treatment . Brain 81:157-190, 1958;.

Figures

Tables

Interactive Graphics

Video

Country-Specific Mortality and Growth Failure in Infancy and Yound Children and Association With Material Stature

Use interactive graphics and maps to view and sort country-specific infant and early dhildhood mortality and growth failure data and their association with maternal

References

Dreschfeld J:  On some of the rarer forms of muscular atrophies . Brain 9:178-195, 1887;.
Ross J, Bury JS: On peripheral neuritis . London, 1893;.
Davies DM:  Recurrent peripheralnerve palsies in a family . Lancet 2:266-268, 1954;.
Ungley CC:  Recurrent polyneuritis in pregnancy and the puerperium affecting three members of a family . J Neurol Psychopathol 14:15-26, 1933;.
Taylor RA:  Heredofamilial mononeuritis multiplex with brachial predilection . Brain 83:113-137, 1960;.
Jacob JC, Andermann F, Robb JP:  Heredofamilial neuritis with brachial predilection . Neurology 11:1025-1033, 1961;.
Gardner JH, Maloney W:  Hereditary brachial and cranial neuritis genetically linked with ocular hypotelorism and syndactly . Neurology 18:278-281, 1968;.
Wyburn-Mason R:  Brachial neuritis occurring in epidemic form . Lancet 2:662-663, 1941;.
Spillane JD:  Localized neuritis of the shoulder girdle . Lancet 2:532-535, 1943;.
Parsonage MJ, Turner JWA:  Neuralgic amyotrophy: The shoulder-girdle syndrome . Lancet 1:973-978, 1948;.
Turner JWA, Parsonage JF:  Neuralgic amyotrophy (paralytic brachial neuritis) with reference to prognosis . Lancet 2:209-212, 1957;.
Magee KR, DeJong RN:  Paralytic brachial neuritis: Discussion of clinical features with review of 23 cases . JAMA 174:1258-1262, 1960;.
Evans HW:  Paralytic brachial neuritis: Report of a case . Lancet 83:251-252, 1963;.
Kennedy WR, Resch JA:  Paralytic brachial neuritis . Lancet 86:459-462, 1966;.
Dejerine J, Sottas J:  Sur la nevrite intestitielle, hypertrophique et progressive de l'enfance . Compt Rend Soc Biol 5:63-96, 1893;.
de Bruyn RS, Stern RO:  A case of the progressive hypertrophic polyneuritis of Dejerine and Sottas, with pathological examination . Brain 52:84-107, 1929;.
Fleming R:  Refsum's syndrome: An unusual hereditary neuropathy . Neurology 7:476-479, 1957;.
Austin JH:  Recurrent polyneuropathies and their corticosteroid treatment . Brain 81:157-190, 1958;.

Correspondence

CME
Accreditation Information
The American Medical Association is accredited by the Accreditation Council for Continuing Medical Education to provide continuing medical education for physicians. The AMA designates this journal-based CME activity for a maximum of 1 AMA PRA Category 1 CreditTM per course. Physicians should claim only the credit commensurate with the extent of their participation in the activity. Physicians who complete the CME course and score at least 80% correct on the quiz are eligible for AMA PRA Category 1 CreditTM.
Note: You must get at least of the answers correct to pass this quiz.
You have not filled in all the answers to complete this quiz
The following questions were not answered:
Sorry, you have unsuccessfully completed this CME quiz with a score of
The following questions were not answered correctly:
Commitment to Change (optional):
Indicate what change(s) you will implement in your practice, if any, based on this CME course.
Your quiz results:
The filled radio buttons indicate your responses. The preferred responses are highlighted
For CME Course: A Proposed Model for Initial Assessment and Management of Acute Heart Failure Syndromes
Indicate what changes(s) you will implement in your practice, if any, based on this CME course.
NOTE:
Citing articles are presented as examples only. In non-demo SCM6 implementation, integration with CrossRef’s “Cited By” API will populate this tab (http://www.crossref.org/citedby.html).
Submit a Comment

Some tools below are only available to our subscribers or users with an online account.

Related Content

Customize your page view by dragging & repositioning the boxes below.