Congenital Cystic Adenomatoid Malformation of the Lung:  Report of a Case and Review of the Literature

BARTHOLINUS first described congenital cystic disease of the lung in 1687,1 but it has become apparent in recent years that acquired cysts of the lung far outnumber the entire group of cyst of congenital origin.2,3 In their classification of congenital pulmonary anomalies, the American College of Chest Physicians⁴ include eight types of cystic lesions, one of the rarest of which is congenital cystic adenomatoid malformation (CCAM).

• A. Cystic Malformation

  1. 1. Solitary cysts

  2. 2. Multiple cysts

  3. 3. Cystic sequestration

  4. 4. Cystic adenomatoid malformation

  5. 5. Diffuse cystic lymphangiectasis

• B. Congenital Pulmonary Cyst

  1. 1. Solitary

     • a. Asymptomatic

     • b. Tension and communicating

  2. 2. Multiple

  3. 3. Cystic bronchiectasis

In 1949, Ch'in and Tang5 reviewed ten cases from the German literature and added one case of their own in the first report in the English language. Although Fischer et all successfully resected this malformation as early as 1943, there has been