THE cardiac anomaly in which the right pulmonary artery originates from the ascending aorta is a rare and usually fatal form of congenital heart disease. This lesion is often associated with a patent ductus arteriosus. Death frequently occurs in early infancy. However, it is a lesion that can be diagnosed during life and corrected with surgery. Twenty-five cases have been described in the literature.1-7 Nine of these patients have undergone surgical procedures with three survivors.1,3-5,7-11
The purpose of this paper is to present four additional cases of aortic origin of the right pulmonary artery including that of one infant who was successfully operated upon at 1 month of age.
Report of Cases
Case 1.—This 24-day-old male infant of Spanish-American extraction was born Jan 19, 1964 to a prima gravida 16-year-old mother after a normal pregnancy and uncomplicated delivery. The birth weight was 3.6 kg (7 lb 15 oz).