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March 1967, Vol 113, No. 3 >
Article | March 1967

Neurofibromatosis in Infancy Presenting With Congenital Stridor FREE

Jeanette Pleasure, MD; Stephen A. Geller, MD
[+] Author Affiliations

Received for publication Sept 6, 1966.

Reprint requests to 100th St and Fifth Ave, New York 10029 (Dr. Geller).


Am J Dis Child. 1967;113(3):390-393. doi:10.1001/archpedi.1967.02090180150018.
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References
Comments

THE OCCURRENCE of von Recklinghausen's disease in an infant is not in itself remarkable, nor is involvement of the larynx in generalized neurofibromatosis noteworthy. A neurofibroma of the larynx causing respiratory distress in an infant with café-au-lait spots is, however, unusual. The Department of Pediatrics of the Mount Sinai Hospital recently had the opportunity to study an infant with von Recklinghausen's disease and persistent stridor caused by a plexiform neurofibroma of the larynx. The child died as a result of complications arising from the laryngeal lesion and came to postmortem examination.

Report of a Case  A 6½-month-old white girl was admitted to the Mount Sinai Hospital for the first and only time in January 1966, with a three-day history of increasing respiratory distress. The infant's mother was a 20-year-old gravida 1 who had an uncomplicated pregnancy and delivery. The birthweight was approximately 3,500 gm (7 lb 12 oz). Noisy respirations

REFERENCES

1 +
ZoBell, D.H.:  Massive Neurofibroma of the Larynx , Laryngoscope 74:233, 1964;.
2 +
Figi, F.A., and Stark, D.B.:  Neurofibroma of the Larynx , Laryngoscope 63:652, 1953;.
3 +
Pung, S., and Hirsch, E.F.:  Plexiform Neurofibromatosis of the Heart and Neck , Arch Path 59:341, 1955;.
4 +
Roget, J., et al:  La maladie de recklinghausen chez le nourrisson , Pediatrie 19:421, 1964;.
5 +
Gibbs, N.M.; Taylor, M.; and Young, A.:  von Recklinghausen's Disease in the Larynx and Trachea of an Infant , J Laryng Otol 71:626, 1957;.
6 +
Stout, A.P.:  Tumors of the Peripheral Nervous System , Atlas of Tumor Pathology , section II, Fascicle 6, p 16, 1949;.
7 +
Russell, D.S., and Rubenstein, L.J.: Pathology of Tumors of the Nervous System , ed 2, London: Edward Arnold Ltd., 1963;.
8 +
Hoover, W.B.:  Benign Tumors of the Larynx , Surg Clin N Amer 20:697, 1940;.
9 +
Aponte, G.E., and Vicens, E.A.:  Neurogenic Tumors of the Larynx , Ann Otol 64:319, 1955;.

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Country-Specific Mortality and Growth Failure in Infancy and Yound Children and Association With Material Stature

Use interactive graphics and maps to view and sort country-specific infant and early dhildhood mortality and growth failure data and their association with maternal

References

1 +
ZoBell, D.H.:  Massive Neurofibroma of the Larynx , Laryngoscope 74:233, 1964;.
2 +
Figi, F.A., and Stark, D.B.:  Neurofibroma of the Larynx , Laryngoscope 63:652, 1953;.
3 +
Pung, S., and Hirsch, E.F.:  Plexiform Neurofibromatosis of the Heart and Neck , Arch Path 59:341, 1955;.
4 +
Roget, J., et al:  La maladie de recklinghausen chez le nourrisson , Pediatrie 19:421, 1964;.
5 +
Gibbs, N.M.; Taylor, M.; and Young, A.:  von Recklinghausen's Disease in the Larynx and Trachea of an Infant , J Laryng Otol 71:626, 1957;.
6 +
Stout, A.P.:  Tumors of the Peripheral Nervous System , Atlas of Tumor Pathology , section II, Fascicle 6, p 16, 1949;.
7 +
Russell, D.S., and Rubenstein, L.J.: Pathology of Tumors of the Nervous System , ed 2, London: Edward Arnold Ltd., 1963;.
8 +
Hoover, W.B.:  Benign Tumors of the Larynx , Surg Clin N Amer 20:697, 1940;.
9 +
Aponte, G.E., and Vicens, E.A.:  Neurogenic Tumors of the Larynx , Ann Otol 64:319, 1955;.

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