0
Article |

Lipoid Proteinosis

ALFRED B. FALK, M.D.; ROLAND S. MEDANSKY, M.D.; PAUL C. TRACY, M.D.; LAWRENCE J. SHOLLER, M.D.
AMA Am J Dis Child. 1958;96(6):727-729. doi:10.1001/archpedi.1958.02060060729014.
Text Size: A A A
Published online

Although lipoid proteinosis is observed primarily in the child, references to this condition in the pediatric literature are scant. The term lipoid proteinosis was first used by Urbach4 in 1932. This, however, was the renaming of this group of cases, as they had been previously called lipoidosis cutis et mucosae.2 In 1924 Wiethe1 had reported the first of these cases as a disease consisting of skin and mucous membrane involvement, but not until 1929 did Urbach and Wiethe3 show their cases to be identical. Their patients showed a hoarseness present almost since birth, with growths involving the mucous membranes and vocal cords. Nodules and plaques occurred on the gums, mucous membranes, floor of the mouth, soft palate, frenulum of the tongue, and uvula. Mucous membranes of the genital and rectal areas were similarly affected. Incidental findings reported by other observers included alopecia of the scalp, loss

Topics

Sign In to Access Full Content

Don't have Access?

Register and get free email Table of Contents alerts, saved searches, PowerPoint downloads, CME quizzes, and more

Subscribe for full-text access to content from 1998 forward and a host of useful features

Activate your current subscription (AMA members and current subscribers)

Purchase Online Access to this article for 24 hours

First Page Preview

View Large
/>
First page PDF preview

Figures

Tables

References

Correspondence

CME
Meets CME requirements for:
Browse CME for all U.S. States
Accreditation Information
The American Medical Association is accredited by the Accreditation Council for Continuing Medical Education to provide continuing medical education for physicians. The AMA designates this journal-based CME activity for a maximum of 1 AMA PRA Category 1 CreditTM per course. Physicians should claim only the credit commensurate with the extent of their participation in the activity. Physicians who complete the CME course and score at least 80% correct on the quiz are eligible for AMA PRA Category 1 CreditTM.
Note: You must get at least of the answers correct to pass this quiz.
You have not filled in all the answers to complete this quiz
The following questions were not answered:
Sorry, you have unsuccessfully completed this CME quiz with a score of
The following questions were not answered correctly:
Commitment to Change (optional):
Indicate what change(s) you will implement in your practice, if any, based on this CME course.
Your quiz results:
The filled radio buttons indicate your responses. The preferred responses are highlighted
For CME Course: A Proposed Model for Initial Assessment and Management of Acute Heart Failure Syndromes
Indicate what changes(s) you will implement in your practice, if any, based on this CME course.
NOTE:
Citing articles are presented as examples only. In non-demo SCM6 implementation, integration with CrossRef’s "Cited By" API will populate this tab (http://www.crossref.org/citedby.html).
Submit a Comment

Multimedia

Some tools below are only available to our subscribers or users with an online account.

Sign In to Access Full Content

Related Content

Customize your page view by dragging & repositioning the boxes below.

Jobs
brightcove.createExperiences();