The congenital formation of a web of skin extending from the mastoid area to the region of the acromion process is unusual, especially when found without developmental anomalies of the cervical portion of the spine.
In 1883 Kobylinski1 described webbing of the skin on the lateral aspects of the neck and suggested its possible relation to congenital short neck. In 1902 Funke2 described this condition in a 15 year old girl, using the term pterygium colli. In his case there were associated abnormalities of the breast and nipples and absence of pubic and axillary hair. Bussière3 in 1902 reported webbing of the neck in a Hindu boy 12 years of age. In 1912 Klippel and Feil4 reported a case in which webbing of the neck was associated with congenital malformation of the cervical part of the spine. Drachter5 in 1923 reported a case in which